Smiling baby sitting on a gray couch, looking to the side.

Hemifacial Microsomia

Personalized treatment restores symmetry, function, and long-term facial balance

What Is Hemifacial Microsomia?

Understanding Hemifacial Microsomia

Hemifacial Microsomia is a congenital condition characterized by underdevelopment of one side of the face due to disruptions in early fetal growth. This asymmetry most commonly affects the jaw, ear, cheek, and surrounding soft tissues, with severity ranging from mild differences to more complex structural involvement. Because children with Hemifacial Microsomia continue to grow and develop, treatment often involves multiple interventions performed at different stages of childhood rather than a single corrective procedure.

Illustration of hemifacial microsomia showing underdevelopment of one side of the face.
Hemifacial Microsomia

Defining Characteristics

Hemifacial Microsomia impacts facial growth and function by altering the balanced development of skeletal and soft tissue structures on one side of the face. These differences may affect chewing, speaking, breathing, and hearing, particularly as a child grows. Management focuses on supporting normal development while addressing functional concerns through carefully timed interventions that evolve with facial growth and maturation.

Facial Asymmetry

Uneven growth of the jaw, cheek, and soft tissues results in visible differences between the two sides of the face.

Ear Abnormalities

The external ear may be small, malformed, or absent, often accompanied by conductive hearing loss.

Jaw Underdevelopment

A smaller lower jaw on one side can affect bite alignment, chewing efficiency, and facial balance.

Soft Tissue Deficiency

Reduced muscle and soft tissue volume may contribute to contour differences and functional limitations.

Hemifacial Microsomia

Pruzansky / Kaban Classification

The Pruzansky–Kaban classification describes the severity of mandibular involvement in hemifacial microsomia and helps guide treatment planning. Type I reflects a small but well-formed mandible, Type IIA a hypoplastic mandible with a functional joint, Type IIB a more underdeveloped mandible with a poorly formed or displaced joint, and Type III near-complete absence of the ramus and temporomandibular joint.

Illustration of hemifacial microsomia Type I showing underdevelopment of one side of the face.

1

Illustration of hemifacial microsomia with a type 2A mandible.

2A

Illustration of hemifacial microsomia with a type 2B mandible.

2B

Child with hemifacial microsomia

3

Illustration of hemifacial microsomia Type I showing underdevelopment of one side of the face.

1

Illustration of hemifacial microsomia with a type 2A mandible.

2A

Illustration of hemifacial microsomia with a type 2B mandible.

2B

Illustration of hemifacial microsomia with a type 3 mandible.

3

Coordinated Pediatric Specialty Care

Children with hemifacial microsomia require comprehensive, coordinated, longitudinal care delivered through a carefully planned treatment approach. Management is guided by facial growth and evolving functional needs, with each evaluation, recommendation, and intervention precisely timed and aligned to support symmetry, jaw function, and hearing. This stepwise approach ensures efficient, consistent care from early childhood through adolescence and long-term follow-up.

Multidisciplinary Care

Children with Hemifacial Microsomia benefit from a coordinated team approach including specialists in:

Craniofacial Surgery
Oral & Maxillofacial Surgery
Genetics
ENT / Otolaryngology
Orthodontics
Speech Therapy
Audiology
Ophthalmology
Pediatrics

Treatment & Care Pathway

father with baby in pediatrician office

Diagnostic Evaluation & Counseling

Comprehensive evaluation helps define the severity of hemifacial microsomia, identify associated conditions, and guide long term treatment planning.

Woman pediatrician is examining little baby.

Hearing Assessment & Treatment

Early hearing evaluation helps identify hearing loss and supports speech, language, and developmental progress through appropriate treatment.

Illustration of staged ear reconstruction for microtia.

Ear Reconstruction

When necessary, ear reconstruction is typically performed around 6 years of age, when ear growth and rib cartilage development are better suited for reconstruction.

Doctor discussing genioplasty options with a young male patient.

Planning for Orthognathic Surgery

Long term monitoring and growth analysis help determine if and when jaw surgery may be beneficial to improve facial symmetry and bite alignment.

Surgical Treatment Options

Illustration of mandibular distraction gradually lengthening an infant lower jaw.

Mandibular Distraction

Mandibular distraction is used in more severe cases of hemifacial microsomia to lengthen the underdeveloped lower jaw and improve symmetry and function. By gradually advancing the jaw on the affected side, this approach supports occlusion and soft tissue balance. Timing is based on severity and growth, with careful planning to achieve stable, predictable outcomes.

Detailed illustration of hemifacial microsomia affecting facial bones and tissues.

Microtia Repair

Microtia repair with a rib graft is a technique used to create a natural appearing ear using the child’s own cartilage. Small sections of rib cartilage are carefully shaped into the framework of an ear and placed beneath the skin to recreate the external ear structure. This approach is typically performed around six years of age, when the ear has reached near adult size and the rib cartilage is sufficiently developed for reconstruction. The result is a durable, long term reconstruction created from the patient’s own tissue.

Two skull models illustrating craniofacial abnormalities in Crouzon Syndrome.

Double Jaw Surgery

Hemifacial microsomia involves asymmetric development of the jaw and facial structures, often affecting occlusion and overall facial balance. Double Jaw surgery allows coordinated repositioning of both the maxilla and mandible to correct asymmetry, level the occlusal plane, and restore more balanced facial proportions. This approach is especially useful in moderate to severe cases where both jaws contribute to the deformity.

Treatment Timeline

Birth

Diagnosis and Specialist Evaluation

3D imaging, hearing assessment, and multidisciplinary planning.

Birth – Age 2

Early Mandibular Distraction (if indicated)

For airway compromise or significant jaw asymmetry in infancy.

Ages 2–4

Speech Therapy Initiated (if indicated)

Early intervention as speech development is monitored.

Ages 6–7

Ear Reconstruction (if indicated)

Rib graft or implant-based reconstruction of the affected ear.

Ages 7–9

Mandibular Distraction or Rib Graft Reconstruction (if indicated)

Approach based on severity and condyle development.

Ages 8–12

Nerve Reconstruction (if indicated)

Facial nerve grafting when functional involvement is present.

Ages 10–12

Phase 1 Orthodontic Treatment (if indicated)

Appliances guide bite and jaw development.

Ages 12–14

Soft Tissue Augmentation (if indicated)

Fat grafting or implants to restore facial volume; severe cases.

Ages 14–16

Pre-Surgical Orthodontics and Planning (if indicated)

Virtual surgical planning and final orthodontic alignment.

Ages 16–18

Orthognathic Surgery (if indicated)

At skeletal maturity; some patients may require additional jaw surgery.

Young adult

Post-Surgical Orthodontics and Long-Term Follow-Up

Experience Matters

“We personally plan your care, perform your surgery, and guide your recovery. No residents, no fellows, no handoffs.

Choosing the right surgical team matters. You should feel informed, comfortable, and confident in every step of the process. At our practice, your care is provided by one of the most highly trained and experienced jaw surgery teams in the country.

When you come to our office, you meet directly with your surgeons. We are the ones who plan your treatment, perform your surgery, see you after surgery, and remain personally available to you throughout your recovery. Unlike larger institutions, your care is not delegated to residents, fellows, or doctors in training. Every critical aspect of your treatment is handled by your surgeons.

Founding Members of the American Society of Orthognathic Surgery

What Our Patients Are Saying

Handsome young man, blue shirt, short hair, smiling
★★★★★

Dr Lee and the team at Northeast Facial are incredible. I was very nervous about my procedure but Dr Lee walked me through it step by step, never once making me feel rushed. Silvanna at the front desk went above and beyond to help me schedule an appointment that worked for me. I would highly recommend NEFOSS!

Stephanie Brown

★★★★★

“I had double jaw surgery done with Dr. Jacob in June 2021. I am extremely happy with my results. No more jaw pain and chewing problems. I also feel much more confident with my new smile. The surgery was definitely well worth it, thanks to Dr. Jacob and his team!”

Amelia Chen

★★★★★

“I would definitely recommend Dr. Jacob and his team at NEFOSS! Dr. Jacob and the team of doctors are very knowledgeable about all aspects of the TMJ process. They are such a nice group of doctors! The office staff is also very helpful and very friendly.”

Tiffany Puopolo

Frequently Asked Questions

Our advanced jaw surgery procedures are designed to enhance your quality of life. With a focus on precision and patient comfort, we ensure optimal results tailored to your unique needs.

Choosing Your Care Team

How important is experience in treating Hemifacial Microsomia?

Hemifacial Microsomia is a complex craniofacial condition that can affect the jaw, ears, facial soft tissues, nerves, airway, and dental development. Treatment often requires careful planning over many years and may involve multiple procedures at different stages of growth. Surgeons and craniofacial teams with extensive experience treating Hemifacial Microsomia are generally better equipped to manage the condition's unique anatomical variations and long-term treatment needs.

What is the difference between private practice and academic or hospital-based care?

In a private practice setting, care is often more streamlined and centered around direct surgeon involvement throughout evaluation, treatment planning, surgery, and follow-up.

In academic or hospital-based environments, care may involve a larger team that includes residents or fellows participating under supervision. Both models can provide excellent care, but families may experience different levels of continuity throughout treatment. At our center, your care is provided directly by your surgeon, without residents or fellows performing surgery.

Who will perform my surgery or procedure?

It is important to understand who is performing each part of your treatment. In some settings, the attending surgeon performs all critical portions of the procedure, while in others trainees may assist or participate under supervision. This should be discussed clearly in advance. At our center, your surgeon performs all critical portions of the procedure.

Will trainees be involved in my care?

Depending on the treatment setting, residents, fellows, or students may be involved in aspects of care. Patients and families should feel comfortable asking about their role and how care is supervised throughout treatment.

At our center, there are no residents or fellows involved in performing surgery.

Who will follow me after treatment or surgery?

Long-term follow-up is an important part of care for many conditions managed at our center. In some practices, post-treatment care may be shared among multiple providers, while in others the surgeon remains closely involved throughout recovery and monitoring. At our center, your surgeon personally follows you throughout recovery and long-term care.

How involved is the surgeon throughout the process?

Comprehensive care includes direct surgical involvement in evaluation, treatment planning, surgery, and long-term follow-up. Consistency throughout the process helps maintain continuity of care.

Understanding Hemifacial Microsomia

What is Pierre Robin Sequence?

Pierre Robin Sequence is a congenital condition that typically begins with a small lower jaw, which causes the tongue to fall backward and partially block the airway. Many children also have a cleft palate. The severity varies considerably from one child to another, and early recognition and appropriate management make a meaningful difference in outcomes.

What is Hemifacial Microsomia?

Hemifacial Microsomia is a congenital condition in which one side of the face develops incompletely before birth. The jaw is most commonly affected, but the condition may also involve the ear, cheek, facial muscles, soft tissues, nerves, and surrounding structures. The severity varies considerably from one individual to another.

What causes Hemifacial Microsomia?

The exact cause is not fully understood. Most cases occur sporadically and are not inherited. Researchers believe that early developmental disruptions affecting blood supply or tissue formation during fetal development may contribute to the condition. In most cases, there is no identifiable action, exposure, or event during pregnancy that caused the condition.

How does Hemifacial Microsomia affect facial growth?

The affected side of the face often grows differently from the unaffected side. This can lead to facial asymmetry involving the jaw, chin, cheeks, and lower face. As a child grows, the degree of asymmetry may become more noticeable, making ongoing monitoring important throughout development.

Does Hemifacial Microsomia affect the ears?

Yes. Ear involvement is common and may range from mild differences in ear shape to significant underdevelopment of the external ear, known as microtia. Some patients also have narrowing or absence of the ear canal, which can affect hearing.

Can hearing be affected?

Yes. Hearing loss is relatively common when the ear canal or middle ear structures are affected. Regular hearing evaluations are important, particularly during childhood when speech and language development are occurring.

Does Hemifacial Microsomia affect breathing?

Some patients have smaller jaw structures that can contribute to airway narrowing. In more severe cases, breathing concerns may be identified during infancy or childhood and require additional evaluation or treatment.

Are both sides of the face ever affected?

Although Hemifacial Microsomia most commonly affects one side of the face, both sides can be involved to varying degrees in some patients. When both sides are affected, the condition may present differently and require individualized treatment planning.

Surgical & Treatment Considerations

What treatments are commonly involved?

Treatment depends on the severity of the condition and the structures involved. Care may include hearing management, orthodontics, jaw reconstruction, mandibular distraction osteogenesis, fat grafting, facial soft tissue augmentation, ear reconstruction, and orthognathic jaw surgery. Not every patient requires every procedure.

When is jaw surgery performed?

The timing depends on the severity of jaw involvement and the patient's age. Some children with significant jaw underdevelopment may benefit from mandibular distraction during childhood. More definitive jaw surgery is often considered after facial growth is largely complete during late adolescence or early adulthood.

What is mandibular distraction osteogenesis?

Mandibular distraction osteogenesis is a technique that gradually lengthens the jaw bone. After a controlled surgical cut is made in the jaw, a distraction device slowly moves the bone segments apart, allowing new bone to form between them. This can improve jaw position, facial balance, and airway function in selected patients.

Will facial asymmetry completely disappear after treatment?

The goal of treatment is to significantly improve facial balance, symmetry, function, and quality of life. Because Hemifacial Microsomia affects multiple tissues and structures, perfect symmetry is not always achievable. Treatment plans focus on creating the best functional and aesthetic outcome possible for each individual patient.

Is ear reconstruction commonly performed?

For patients with microtia or significant ear differences, ear reconstruction may be considered. The timing and technique depend on the patient's age, anatomy, hearing status, and overall treatment plan. Ear reconstruction is often coordinated with other aspects of craniofacial care.

Will orthodontic treatment be needed?

Many patients benefit from orthodontic treatment because differences in jaw growth frequently affect bite alignment. Orthodontics is often coordinated with surgical planning to achieve the best long-term functional result.

Long-Term Monitoring & Growth

Will my child need long-term follow-up?

Long-term follow-up typically includes monitoring facial growth, jaw development, hearing, dental development, bite alignment, airway function, and overall facial symmetry. Treatment recommendations may change as growth occurs and individual needs evolve.

Does Hemifacial Microsomia get worse with growth?

The condition itself does not worsen, but differences in growth between the affected and unaffected sides may become more apparent over time. Regular evaluation helps determine whether treatment should be adjusted as the child develops.

Can individuals with Hemifacial Microsomia live full lives?

Yes. Most individuals with Hemifacial Microsomia live healthy, active lives. Early evaluation, coordinated treatment planning, and appropriate management of hearing, dental, airway, and facial growth concerns can help patients achieve excellent long-term outcomes.

Will additional procedures be needed later in life?

Some patients require staged treatment throughout childhood and adolescence, while others need only limited intervention. The need for future procedures depends on growth patterns, severity, functional concerns, and personal treatment goals.

Can children with Hemifacial Microsomia live normal lives?

Yes. Most children with Hemifacial Microsomia grow up to live healthy, active, and fulfilling lives. The condition affects facial development, but with appropriate monitoring and treatment when needed, many children participate fully in school, sports, social activities, and everyday life. Outcomes depend on the severity of the condition and any associated concerns involving hearing, breathing, dental development, or facial growth. Early evaluation and coordinated care help ensure that children receive the support they need as they grow and develop.

Traveling & Out-Of-Town Patients

Do families travel to your center for treatment?

Yes. We regularly care for children, adolescents, and adults who travel from outside the region for specialized craniofacial and jaw surgery evaluation and treatment.

How long do families typically need to stay near your center?

The length of stay depends on the procedure being performed. For consultations and treatment planning, most families can return home shortly after their visit. Following procedures such as mandibular distraction, jaw surgery, or reconstructive procedures, patients typically remain locally until their surgeon confirms that healing is progressing appropriately and travel is safe. Specific timelines vary based on the procedure and individual recovery.

Is driving home different from flying?

Yes. Ground travel is often approved sooner than air travel following certain craniofacial and jaw procedures. Your surgeon will provide individualized recommendations regarding both driving and flying based on the procedure performed and your recovery progress.

What can families expect during evaluation and treatment planning?

Evaluation includes a detailed review of facial growth, jaw anatomy, hearing status, dental development, airway function, prior treatments, and imaging studies. Families receive a personalized treatment plan that outlines current needs, anticipated future treatment, and the timing of any recommended procedures. For out-of-town patients, follow-up care and travel logistics are discussed in detail to help make treatment as smooth as possible.

What can families expect during evaluation and treatment planning?

Evaluation at our center includes a comprehensive assessment of facial growth, jaw development, airway function, hearing, dental development, and overall facial symmetry. Imaging studies and previous treatment records are carefully reviewed to better understand the individual's anatomy and treatment needs.

Families receive a personalized treatment plan that outlines current concerns, potential future procedures, and the timing of any recommended interventions. Because Hemifacial Microsomia can affect multiple structures and continues to evolve with growth, treatment planning often focuses not only on immediate needs but also on long-term developmental goals. Families have the opportunity to discuss all available options, ask questions, and gain a clear understanding of what to expect at each stage of care.

Young child holding flowers outdoors
Take the first step of your journey.

Schedule a private consultation today

Scroll to Top